Pediatric restrictive Cardiomyopathy presenting with congestive heart failure: Rare case report and literature review

Akhil Mehrotra 1, *, Mohammad Shaban 2, Faiz Illahi Siddiqui 2 and Naveen Chandra 3

1 Pediatric and Adult Cardiology, Prakash Heart Station, Nirala Nagar, Lucknow, UP, India.
2 Prakash Heart Station, Nirala Nagar, Lucknow, UP, India.
3 Lucknow, UP, India.
 
Case Study
World Journal of Biology Pharmacy and Health Sciences, 2024, 20(01), 216–236.
Article DOI: 10.30574/wjbphs.2024.20.1.0703
Publication history: 
Received on 22 August 2024; revised on 05 October 2024; accepted on 08 October 2024
 
Abstract: 
Restrictive cardiomyopathy (RCM) is an uncommon form of cardiomyopathy and is characterized by impaired diastolic filling of the ventricles due to increased myocardial stiffness and a normal ventricular systolic functions. In India, RCM is frequently observed in the young and endemic endomyocardial diseases are seen  in a significant number of cases. RCM is the least common of all the cardiomyopathies among pediatric patients. RCM has a poor prognosis and commonly requires a cardiac transplant.
We are reporting here a case of seven-year-old female child presenting with recurrent chest infections and congestive heart failure since early childhood.
 
Keywords: 
Restrictive cardiomyopathy; Restrictive cardiomyopathy of infiltrative variety; Pediatric restrictive cardiomyopathy; Diastolic heart failure; Dilated pulmonary artery
 
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